Event Videos

https://pubmed.ncbi.nlm.nih.gov/35444966/ NAFLD

Front Pediatr. 2022 Apr 4;10:846273.
doi: 10.3389/fped.2022.846273. eCollection 2022.

Stratification by Non-invasive Biomarkers of Non-alcoholic Fatty Liver Disease in Children

Yiyoung Kwon 1, Eun Sil Kim 1, Yon Ho Choe 1, Mi Jin Kim 1

Abstract
Background: The spectrum of non-alcoholic fatty liver disease (NAFLD) ranges from isolated hepatic steatosis to non-alcoholic steatohepatitis to fibrosis. We aimed to introduce useful biomarkers released during liver inflammation and fibrogenesis that are easy to use in outpatient clinic and adjust to children to evaluate each NAFLD stage without biopsy.

Published on: 
Apr-2022

https://pubmed.ncbi.nlm.nih.gov/35393118/ Biliary atresia

J Pediatr Surg. 2022 Mar 15;S0022-3468(22)00216-0.
doi: 10.1016/j.jpedsurg.2022.03.009.Online ahead of print.

Progress in living donor liver transplantation for biliary atresia and challenges faced: A thirty-year single institutional experience

Tatsuya Okamoto 1, Hideaki Okajima 2, Eri Ogawa 3, Mari Sonoda 3, Elena Yukie Uebayashi 3, Takashi Ito 3, Satoru Seo 3, Koichiro Hata 3, Toshihiko Masui 3, Kojiro Taura 3, Shinji Uemoto 4, Etsurou Hatano 3

Abstract

Published on: 
Mar-2022

https://pubmed.ncbi.nlm.nih.gov/35442241/ NAFLD

J Pediatr Gastroenterol Nutr. 2022 Apr 20.
doi: 10.1097/MPG.0000000000003461.Online ahead of print.

Insight into the Adolescent Patient Experience with Nonalcoholic Fatty Liver Disease

Sanita L Ley 1 2, Katherine M Kidwell 1 3, Tori R Van Dyk 4, Sarah Orkin 2 5, Cathleen Odar Stough 6, Taylor Howarth 1, Amy R Goetz 1 7, Stavra A Xanthakos 2 5, Kristin Bramlage 2 4, Marialena Mouzaki 2 5, Ana Catalina Arce-Clachar 2 5, Meg H Zeller 1 2

Abstract

Published on: 
Apr-2022

https://pubmed.ncbi.nlm.nih.gov/35368683/ Neimann-Pick

Front Genet. 2022 Mar 18;13:867413.
doi: 10.3389/fgene.2022.867413. eCollection 2022
.
The Presence of Vacuolated Kupffer Cells Raises a Clinical Suspicion of Niemann-Pick Disease Type C in Neonatal Cholestasis

Neng-Li Wang 1, Lian Chen 2, Yi Lu 1, Xin-Bao Xie 1, Jing Lin 3, Kuerbanjiang Abuduxikuer 1, Jian-She Wang 1

Abstract

Published on: 
Mar-2022

https://pubmed.ncbi.nlm.nih.gov/35442238/ Metabolic

J Pediatr Gastroenterol Nutr. 2022 Apr 20.
doi: 10.1097/MPG.0000000000003452.Online ahead of print
.
Long-term Sebelipase Alfa Treatment in Children and Adults With Lysosomal Acid Lipase Deficiency

Barbara K Burton 1, Alejandra Consuelo Sanchez 2, Maria Kostyleva 3, Ana Maria Martins 4, Sachin Marulkar 5, Florian Abel 5, Ivo Barić 6
Abstract

Objectives: Sebelipase alfa is approved for treatment of lysosomal acid lipase deficiency (LAL-D). This single-arm, open-label study (NCT02112994) evaluated sebelipase alfa efficacy and safety in patients with LAL-D.

Published on: 
Apr-2022

https://pubmed.ncbi.nlm.nih.gov/35442235/ Acute liver failure

J Pediatr Gastroenterol Nutr. 2022 Apr 20.
doi: 10.1097/MPG.0000000000003448.Online ahead of print
.
Outcomes Analyses of Pediatric Acute Liver Failure Subjects Listed for Liver Transplantation

Sakil S Kulkarni 1, Charles W Goss 2, Adeel S Khan 3, Michelle L Nadler 1, Janis M Stoll 1, Maria B Doyle 3, Yumirle P Turmelle 1, David A Rudnick 1 4

Abstract

Background: We characterized recent outcomes in US pediatric acute liver failure (PALF) subjects listed for liver transplantation (LT) using the Scientific Registry of Transplant Recipients (SRTR) database.

Published on: 
Apr-2022

https://pubmed.ncbi.nlm.nih.gov/35412509/ Acute liver failure

Pediatr Crit Care Med. 2022 Apr 12.
doi: 10.1097/PCC.0000000000002962.Online ahead of print.

Transcranial Doppler Ultrasonography in Children With Acute Liver Failure and Severe Hepatic Encephalopathy

Vladimir L Cousin 1, Ramy Charbel 1, Narjess Ghali 1, Clémence Marais 1, Pierre Tissières 1 2

Abstract

Objectives: To report our single-center use of transcranial Doppler (TCD) for noninvasive neuromonitoring in pediatric patients with acute liver failure (ALF).

Design: Retrospective cohort from January 2016 to June 2019.
Setting: PICU in Bicêtre Hospital, Assistance Publique- Hôpitaux de Paris (AP-HP), a national referral center for pediatric liver transplantation.

Published on: 
Apr-2022

https://pubmed.ncbi.nlm.nih.gov/35328311/ Hepatoblastoma

Case Reports

Diagnostics (Basel). 2022 Mar 20;12(3):758.
doi: 10.3390/diagnostics12030758.

Fetal Pancreatic Hamartoma Associated with Hepatoblastoma-An Unusual Tumor Association

Valentin Varlas 1 2, Oana Neagu 3, Andreea Moga 4, Radu Bălănescu 2 4, Roxana Bohiltea 1 2, Radu Vladareanu 2 5, Laura Balanescu 2 4

Abstract

Published on: 
Mar-2022

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