https://www.ncbi.nlm.nih.gov/pubmed/31540390
J Clin Med. 2019 Sep 18;8(9). pii: E1481. doi: 10.3390/jcm8091481.
Hepatobiliary Complications in Children with Sickle Cell Disease: A Retrospective Review of Medical Records from 616 Patients.
Allali S1,2,3, de Montalembert M4,5, Brousse V6, Heilbronner C7, Taylor M8, Brice J9, Manzali E10, Garcelon N11, Lacaille F12.
Abstract
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https://www.ncbi.nlm.nih.gov/pubmed/31555573 PFIC
Pediatr Gastroenterol Hepatol Nutr. 2019 Sep;22(5):479-486. doi: 10.5223/pghn.2019.22.5.479. Epub 2019 Sep 11.
Novel ATP8B1 Gene Mutations in a Child with Progressive Familial Intrahepatic Cholestasis Type 1.
Rhee ES1, Kim YB1, Lee S1, Oh SH1, Lee BH1, Kim KM1, Yoo HW1.
Abstract
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https://www.ncbi.nlm.nih.gov/pubmed/31549332
Dig Dis Sci. 2019 Sep 23. doi: 10.1007/s10620-019-05834-w. [Epub ahead of print]
Congenital Portosystemic Shunts in Children: Associations, Complications, and Outcomes.
DiPaola F1, Trout AT2,3, Walther AE4, Gupta A5, Sheridan R5, Campbell KM6, Tiao G7, Bezerra JA6, Bove KE5, Patel M2,3, Nathan JD7.
Abstract
BACKGROUND:
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https://www.ncbi.nlm.nih.gov/pubmed/31559303 Wilson Disease
World J Clin Cases. 2019 Sep 6;7(17):2630-2636. doi: 10.12998/wjcc.v7.i17.2630.
Wilson disease associated with immune thrombocytopenia: A case report and review of the literature.
Ma TJ1, Sun GL1, Yao F1, Yang ZL2.
Abstract
BACKGROUND:
Wilson disease (WD) is a genetic disorder of hepatic copper excretion, leading to copper accumulation in various tissues. The manifestations are quite variable, and hemolytic anemia is the most common hematological presentation. WD associated with thrombocytopenia is very rare.
CASE SUMMARY:
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https://www.ncbi.nlm.nih.gov/pubmed/31550050 Chronic liver disease
Cochrane Database Syst Rev. 2019 Sep 24;9:CD010546. doi: 10.1002/14651858.CD010546.pub2.
Band ligation versus beta-blockers for primary prophylaxis of oesophageal variceal bleeding in children with chronic liver disease or portal vein thrombosis.
Gana JC1, Cifuentes LI, Gattini D, Villarroel Del Pino LA, Peña A, Torres-Robles R
Abstract
BACKGROUND:
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https://www.ncbi.nlm.nih.gov/pubmed/31563247 Liver Transplant
Transplant Proc. 2019 Oct;51(8):2793-2797. doi: 10.1016/j.transproceed.2019.03.079.
Outcomes of 50 Cases of Pediatric Liver Transplantation for Intrapulmonary Shunt While Considering the Deteriorated Prognosis of Severe Intrapulmonary Shunt Patients.
Hirata Y1, Sakamoto S2, Yoshimura S1, Takeda M1, Uchida H1, Shimizu S1, Kitamura M3, Irie R4, Miyazaki O3, Yoshioka T4, Nosaka S3, Kasahara M1.
Abstract
BACKGROUND:
Intrapulmonary shunt (IPS) is recognized in 10% of chronic liver disease patients. Liver transplantation (LT) is associated with a high risk of morbidity and mortality in patients with IPS.
PATIENTS AND METHODS:
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https://www.ncbi.nlm.nih.gov/pubmed/31553814 Neonatal cholestasis
Hepatology. 2019 Sep 25. doi: 10.1002/hep.30959. [Epub ahead of print]
Crigler-Najjar syndrome type 1: pathophysiology, natural history, and therapeutic frontier.
Strauss KA1,2,3, Ahlfors CE4, Soltys K5, Mazareigos GV5, Young M1, Bowser LE1, Fox MD1,6,7, Squires JE8, McKiernan P9, Brigatti KW1, Puffenberger EG1, Carson VJ1, Vreman HJ10.
Abstract
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https://www.ncbi.nlm.nih.gov/pubmed/31571364 Alagille syndrome
Pediatr Transplant. 2019 Sep 30:e13579. doi: 10.1111/petr.13579. [Epub ahead of print]
Living donor liver transplantation in Alagille syndrome-Single center experience from south Asia.
Valamparampil JJ1, Reddy MS1, Shanmugam N1, Vij M1, Kanagavelu RG1, Rela M1,2.
Abstract
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https://www.ncbi.nlm.nih.gov/pubmed/31555572 NAFLD
Pediatr Gastroenterol Hepatol Nutr. 2019 Sep;22(5):470-478. doi: 10.5223/pghn.2019.22.5.470. Epub 2019 Sep 11.
Role of Soluble Adiponectin Receptor 2 in Non-Alcoholic Fatty Liver Disease in Children.
Aksoy GK1, Artan R2, Aksoy C3, Özdem S4, Atalay A2, Yılmaz A2.
Abstract
PURPOSE:
The incidence of non-alcoholic fatty liver disease (NAFLD) in children is gradually increasing. The aim of this study was to investigate the use of serum adiponectin and soluble adiponectin receptor 2 (soluble Adipo R2) levels for the diagnosis of fatty liver disease in obese and overweight children.
METHODS:
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https://www.ncbi.nlm.nih.gov/pubmed/31572038 Thalessemia
J Blood Med. 2019 Sep 17;10:323-334. doi: 10.2147/JBM.S186362. eCollection 2019.
Thalassemia and hepatocellular carcinoma: links and risks.
Marsella M1, Ricchi P2.
Abstract
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