https://www.ncbi.nlm.nih.gov/pubmed/29181760
Wilson disease

J Mol Neurosci. 2017 Nov 28. doi: 10.1007/s12031-017-0997-7. [Epub ahead of print]

Liu M, Jin M, Chen X, Wan B, Guo Y, Sheng M, Chen L, Zhao L, Huang D, Li Y.

Abstract

https://www.ncbi.nlm.nih.gov/pubmed/29183422

S Afr Med J. 2017 Nov 6;107(10):12130.
Tyraskis A, Durkin N, Davenport M.

Abstract
Congenital vascular anomalies of the liver include a range of malformations of the portal venous, hepatic arterial and venous systems. Congenital portosystemic shunts and arteriovenous malformations make up the two most frequent such malformations. While infantile haemangiomas of the liver, endothelial tumours characterised by vascular proliferation should also be considered, as a proportion of them form prenatally. Evidence to support treatment strategies for these infants and children has been mainly based on small case series. In this review, we explore classification, clinical presentation, investigation and treatment strategies.

https://www.ncbi.nlm.nih.gov/pubmed/29183423
Biliary atresia

S Afr Med J. 2017 Nov 6;107(10):12131.

De Maayer T, Lala SG, Loveland J, Okudo G, Mohanlal R, Hajinicolaou C.

Abstract

BACKGROUND:
Without timely surgical intervention, most children with biliary atresia (BA) are not expected to live beyond 2 years of age. The initial intervention, the Kasai hepatoportoenterostomy (KPE), aims to achieve biliary drainage. Liver transplantation (LT) is performed if jaundice fails to clear or when biliary cirrhosis occurs. In under-resourced South African (SA) academic state hospitals, KPE procedures are the standard of care for the majority of children with BA, but LT is becoming more routinely available.

OBJECTIVES: