Biliary Atresia

Neonatal cholestasis : How do I approach?

Source Event :Case discussions in Pediatric Liver Diseases organised by Children's Liver Foundation and Indian Academy of pediatric, Mumbai on 14th and 15th December 2013.
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Presented by
Dr Avinash Khade
Moderated by
Dr S K Yachha
Panelists
Dr Malathi Sathiyasekaran
Dr Girish Gupte
Dr Ashley D'Cruz

Timing of Kasai Procedure for Biliary Atresia: An Analysis of the Pediatric National Surgical Quality Improvement Program Database

Timing of Kasai Procedure for Biliary Atresia: An Analysis of the Pediatric National Surgical Quality Improvement Program Database

Systematic review of the mechanism and assessment of liver fibrosis in biliary atresia

Primary liver transplantation vs transplant after Kasai portoenterostomy in children with biliary atresia: A retrospective Brazilian single-center cohort

Effect of medium chain triglycerides enriched formula on growth of biliary atresia patients after Kasai portoenterostomy

Role of cholinergic innervation in biliary remnants of patients with biliary atresia

Long-term clinical and socioeconomic outcomes of children with biliary atresia

Diagnostic and prognostic value of the gut microbiota and its metabolite butyrate in children with biliary atresia

Expedited Laparoscopic Cholangiogram and Liver Biopsy in the Workup of Biliary Atresia

Prophylactic Antibiotics to Prevent Cholangitis in Children with Biliary Atresia After Kasai Portoenterostomy: A Meta-Analysis

A new criterion including the aspartate aminotransferase-to-platelet ratio index and liver and spleen stiffness to rule out varices needing treatment in children with biliary atresia

Development and validation of a model for early diagnosis of biliary atresia

A fetal wound healing program after intrauterine bile duct injury may contribute to biliary atresia

A fetal wound healing program after intrauterine bile duct injury may contribute to biliary atresia

Prophylactic Antibiotics to Prevent Cholangitis in Children with Biliary Atresia After Kasai Portoenterostomy: A Meta-Analysis

Cytomegalovirus in biliary atresia is associated with increased pretransplant death, but not decreased native liver survival

Early bile drainage improves native liver survival in biliary atresia without cholangitis

Age at surgery and native liver survival in biliary atresia: a systematic review and meta-analysis

Kasai Portoenterostomy at a Slightly Delayed Age and Native Liver Survival in Children With Biliary Atresia: Single Center Experience

Development of liver inflammatory injury in biliary atresia: from basic to clinical research

Treatment of intractable cholangitis in children with biliary atresia: Impact on outcome

Plasticity between ILC2 subsets and amphiregulin expression regulate epithelial repair in biliary atresia

Age at surgery and native liver survival in biliary atresia: a systematic review and meta-analysis

The Impact of Thrombophilic Factors on Disease Progression in Children with Biliary Atresia-A Single-Centre Cohort Study

Predictors of biliary atresia outcome: Saudi National Study (2000 - 2018)

Liver-restricted deletion of the biliary atresia candidate gene Pkd1l1 causes bile duct dysmorphogenesis and ciliopathy.

Serum FGF19 predicts outcomes of Kasai portoenterostomy in biliary atresia.

The presence of high-risk varices after sclerotherapy in biliary atresia

Current and emerging adjuvant therapies in biliary atresia

Current and emerging adjuvant therapies in biliary atresia

Peri-Operative Liver Fibrosis and Native Liver Survival in Pediatric Patients with Biliary Atresia: A Systematic Review and Meta-Analysis

Serum Bile Acids as a New Prognostic Biomarker in Biliary Atresia Following Kasai Portoenterostomy

Identification of Hub Genes and Immune Infiltration in Pediatric Biliary Atresia by Comprehensive Bioinformatics Analysis

Progress in living donor liver transplantation for biliary atresia and challenges faced: A thirty-year single institutional experience

Long-term outcomes of biliary atresia patients surviving with their native livers

The Risk of Variceal Hemorrhage and Pre-Transplant Mortality in Children with Biliary Atresia

Quantification of Maternal Microchimeric Cells in the Liver of Children with Biliary Atresia

Newborn Screening for Biliary Atresia: a Review of Current Methods

Serum Proteomics Uncovers Biomarkers of Clinical Portal Hypertension in Children With Biliary Atresia

Body composition correlates with laboratory parameters and disease severity in infants with biliary atresia

Characteristics of the Gut Microbiome and IL-13/TGF-β1 Mediated Fibrosis in Post-Kasai Cholangitis of Biliary Atresia

Malnutrition in Biliary Atresia: Assessment, Management and Outcomes

Effect and mechanism of vitamin D activation disorder on liver fibrosis in biliary atresia

Identification of a wide spectrum of ciliary gene mutations in nonsyndromic biliary atresia patients implicates ciliary dysfunction as a novel disease mechanism

Biliary organoids uncover delayed epithelial development and barrier function in biliary atresia

Analysis of Cholangitis Rates with Extended Perioperative Antibiotics and Adjuvant Corticosteroids in Biliary Atresia

Early Motor Repertoire in Infants with Biliary Atresia: A Nationwide Prospective Cohort Study

Liver Immune Profiling Reveals Pathogenesis and Therapeutics for Biliary Atresia

Combination of Gamma-Glutamyl Transferase and Liver Stiffness Measurement for Biliary Atresia Screening at Different Ages: A Retrospective Analysis of 282 Infants

Beta-amyloid Deposition Around Hepatic Bile Ducts Is a Novel Pathobiological and Diagnostic Feature of Biliary Atresia

Diagnostic Yield of Newborn Screening for Biliary Atresia Using Direct or Conjugated Bilirubin Measurements

Exome Sequencing in Individuals with Isolated Biliary Atresia

Long-Term Neurodevelopmental Outcomes in Children with Biliary Atresia.

Direct Health Care Costs, Health Services Utilization and Outcomes of Biliary Atresia: A Population-Based Cohort Study.

A paradigm shift in the intention-to-transplant children with biliary atresia: Outcomes of 101 cases and a review of the literature

Cystic biliary atresia with paucity of bile ducts and gene mutation in KDM6A: a case report

Spleen and Liver Stiffness to Detect Esophageal Varices in Children with Biliary Atresia

Gene Expression Signatures Associated With Survival Times of Pediatric Patients With Biliary Atresia Identify Potential Therapeutic Agents.

Increased serum glypican-3 is associated with liver stiffness and hepatic dysfunction in children with biliary atresia.

Central line-associated bloodstream infection among children with biliary atresia listed for liver transplantation.

Identification of PKD1L1 Gene Variants in Children with the Biliary Atresia Splenic Malformation Syndrome.

A Phase I/IIa Trial of Intravenous Immunoglobulin Following Portoenterostomy in Biliary Atresia.

Acute-on-chronic liver failure in children with biliary atresia awaiting liver transplantation.

Liver fibrosis in biliary atresia.

Outcome of biliary atresia among Saudi children: A tertiary care center experience.

The effects of Kasai procedure on living donor liver transplantation for children with biliary atresia.

Impact of Steroid Therapy on Early Growth in Infants with Biliary Atresia: The Multicenter Steroids in Biliary Atresia Randomized Trial.

Clinical Consequences of Cardiomyopathy in Children with Biliary Atresia Requiring Liver Transplantation.

CYP7A1 expression in hepatocytes is retained with upregulated fibroblast growth factor 19 in pediatric biliary atresia

Liver transplant score for prediction of biliary atresia patients' survival following Kasai procedure

Neurodevelopmental Outcome of Young Children with Biliary Atresia and Native Liver: Results from the ChiLDReN Study

Province-Wide Biliary Atresia Home Screening Program in British Columbia: Evaluation of First Two Years

BILIARY ATRESIA: Clinical and Research Challenges for the 21st Century

Durable Clinical and Immunologic Advantage of Living Donor Liver Transplantation in Children

Waiting list mortality of young patients with biliary atresia: Competing risk analysis of an Eurotransplant registry-based cohort

Outcomes of Kasai hepatoportoenterostomy in children with biliary atresia in Johannesburg, South Africa

Quality of life of biliary atresia after living donor liver transplant in Japan

Biliary Complications after Hepatic Trauma in Children

Molecular signature of active fibrogenesis prevails in biliary atresia after successful portoenterostomy.

The dendritic cell-Th17-macrophage axis controls cholangiocyte injury and disease progression in murine and human biliary atresia

Early Post-Hepatoportoenterostomy Predictors of Native Liver Survival in Biliary Atresia

Vitamin D Levels in Infants With Biliary Atresia: Pre- and Post-Kasai Portoenterostomy

Home-Based Screening for Biliary Atresia Using Infant Stool Color Cards in Canada: Quebec Feasibility Study.

Effectiveness of Enteral Versus Oral Nutrition With a Medium-Chain Triglyceride Formula to Prevent Malnutrition and Growth Impairment in Infants With Biliary Atresia

Complications and Quality of Life in Long-Term Survivors of Biliary Atresia with Their Native Livers

Expression in Liver Tissue of Biliary Atresia: A New Perspective in Etiopathogenesis

Recent Trends in the Diagnosis and Management of Biliary Atresia in Developing Countries

Living Related Liver Transplantation for Biliary Atresia in the Last 5 years: Experience from the First Liver Transplant Program in India

Biliary Atresia Is Associated With Hypertension

Biliary Atresia: Clinical Lessons Learned

Progression to high-risk gastroesophageal varices in children with biliary atresia with low-risk signs at first endoscopy

Factors Determining δ-Bilirubin Levels in Infants With Biliary Atresia

Use of Lactobacillus casei rhamnosus to Prevent Cholangitis in Biliary Atresia After Kasai Operation

Cost-effective analysis of screening for biliary atresia with the stool color card

Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with Biliary Atresia

Points to be considered when applying FibroScan S probe in children with biliary atresia

Medical status of 219 children with Biliary Atresia surviving long-term with their native livers: results from a North American multicenter consortium

Experience with endoscopic management of high-risk gastroesophageal varices, with and without bleeding, in children with Biliary Atresia.

International Incidence and Outcomes of Biliary Atresia

Continuous 13C Methacetin Breath Test Differentiates Biliary Atresia from other Causes of Neonatal Cholestasis: Results of a Pilot Study

α-SMA Overexpression Associated With Increased Liver Fibrosis in Infants With Biliary Atresia.

Developmental assessment of infants with biliary atresia: differences between boys and girls.

Identification of Serum Protein Biomarkers in Biliary Atresia by Mass Spectrometry and Enzyme-linked Immunosorbent Assay.

Intracranial hemorrhage associated with vitamin K-deficiency bleeding in patients with biliary atresia: focus on long-term outcomes

Biliary Atresia

What is Biliary Atresia (BA)?

Bile is a digestive juice secreted from the liver. Bile passes into the intestine through a tube like structure which is called bile duct. Bile juice is important for the digestion of fat in food and for absorption of fat soluble vitamins. Poor development of the bile duct is called Biliary Atresia. This can lead to cholestatic (direct) jaundice or liver damage.

How common is Biliary Atresia?

Biliary Atresia occurs in 1 in 10,000 to 20,000 live births. It is one of the commonest causes of neonatal jaundice.

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